2
1. A lung transplant does not cure CF, but the transplanted lungs do not contain the CF genes. Although the new lungs do not contain CF, the sinuses, pancreas, intestines, sweat glands, and reproductive tract do. The new lungs are more susceptible to infection because of the immunosuppressive therapy that must be given post-transplant. Immunosuppressive drugs make it difficult for the body to fight infection, which can lead to lung damage.
2. A lung transplant does not cure CF, but it does offer the client an opportunity to live a longer life. The concerns are that, after the lung transplant, the child is at risk for rejection of the new organ and for development of secondary infections because of the immunosuppressive therapy.
3. The lung transplant does not reverse the damage that has been done to the child ' s other organs, but it does offer a chance of a longer life.
4. The average life span of a client with CF has risen over the years with the daily regimens of CPT, exercise, medications, and highcalorie, high-protein diets.
TEST-TAKING HINT: Answer 4 can be eliminated because of the word "only." There are very few times in health care when an answer will be "only." Answers 1 and 3 can be eliminated if the test taker has a basic knowledge of the pathophysiology of CF.
3
Clients with cystic fibrosis commonly die from respiratory problems. The mucus in the lungs is tenacious and difficult to expel, leading to lung infections and interference with oxygen and carbon dioxide exchange. The client will likely need supplemental oxygen and respiratory treatments to maintain adequate gas exchange, as identified by the oximeter reading. The child will be on bed rest due to respiratory distress. However, although blood gases will probably be prescribed, the oximeter readings will be used to determine oxygen deficit and are, therefore, more of a priority. A diet high in calories, proteins, and vitamins with pancreatic granules added to all foods ingested will increase nutrient absorption and help the malnutrition; however, this intervention is not the priority at this time. Inserting an IV to administer antibiotics is important, and can be done after ensuring adequate respiratory function.